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. 2019 Mar 8;7(5):e00617. doi: 10.1002/mgg3.617

Table 4.

The demographic data and ophthalmologic characteristics of 17 Taiwanese patients with MPS IV

No. MPS type Gender Age (years) Right eye or left eye Visual acuity Sphere Cylinder Axis of cylinder Refraction (spherical equivalent) Amblyopia Corneal opacity Lens opacity Optic disc IOP (mmHg) Retinal appearance VEP
IV‐1 IVA M 1.1 R Follow light +0.5 −1.5 180 −0.25 N + Normal Normal ‐ Normal ‐
L Follow light +0.5 −1.5 180 −0.25
IV‐2 IVA M 5.6 R 0.2 (6/30) +3.0 −3.0 13 +1.50 N + Normal Normal 20.1 Normal ‐
L 0.1 (6/60) 0 +3.0 80 +1.50 Y 17.5
IV‐3 IVA M 5.8 R 0.6 (6/10) 0 +3.0 89 +1.50 N + Normal Normal ‐ Normal ‐
L 0.6 (6/10) +0.5 +2.25 91 +1.63
IV‐4 IVA F 6.4 R 0.2 (6/30) +2.5 +2.5 85 +3.75 N + Nuclear sclerosis Normal 21 Normal ‐
L 0.3 (6/20) +2.5 +2.5 90 +3.75 18
IV‐5 IVA F 6.5 R 0.4 (6/15) −0.75 −1.5 1 −1.50 N + Normal Normal ‐ Normal ‐
L 0.4 (6/15) 0 −0.75 25 −0.38
IV‐6 IVA M 7.2 R 0.4 (6/15) +0.75 +2.5 90 +2.00 Y + Normal Normal 17 Normal ‐
L 0.4 (6/15) +0.75 +2.5 84 +2.00 15
IV‐7 IVA M 9.0 R 0.5 (6/12) +0.25 +0.25 52 +0.38 N + Normal Normal ‐ Normal ‐
L 0.7 (6/8.6) +0.25 +1.75 37 +1.13
IV‐8 IVA F 10.9 R 1.0 (6/6) +0.25 −0.75 162 −0.13 N + Normal Normal ‐ Normal ‐
L 1.0 (6/6) +0.5 −1.25 180 −0.13
IV‐9 IVA M 11.6 R 0.6 (6/10) −1.0 −0.5 110 −1.25 N Clear Normal Normal ‐ Normal ‐
L 0.6 (6/10) −1.0 −0.25 73 −1.13
IV‐10 IVA F 13.6 R 0.3 (6/20) +3.5 −5.0 170 +1.00 N + Normal Normal ‐ Normal ‐
L 0.4 (6/15) +4.5 −5.0 5 +2.00
IV‐11 IVA F 14.2 R 0.3 (6/20) +2.5 −3.5 169 +0.75 Y + Normal Normal ‐ Normal ‐
L 0.4 (6/15) +3.0 −4.5 177 +0.75
IV‐12 IVA F 15.7 R 0.3 (6/20) +1.0 −1.75 140 +0.13 N + Normal Normal 26.9 Normal ‐
L 0.9 (6/6.7) −0.25 −0.75 26 −0.63 27
IV‐13 IVA F 15.8 R 0.5 (6/12) +3.0 −3.0 180 +1.50 N ++ Normal Normal ‐ Vitreous opacities ‐
L 0.4 (6/15) +6.0 −5.0 175 +3.50
IV‐14 IVA M 15.9 R 1.0 (6/6) +2.25 +1.00 65 +2.75 N + Normal Normal 15.2 Normal Normal
L 0.9 (6/6.7) +2.25 +1.5 98 +3.00 14.3
IV‐15 IVA F 19.2 R 0.8 (6/7.5) −2.25 −2.25 150 −3.38 N + Normal Cupped 0.5 cup:disc 25.1 Normal ‐
L 0.4 (6/15) −1.75 −1.75 55 −2.63 24.4
IV‐16 IVA M 25.5 R 0.5 (6/12) −0.5 −1.5 170 −1.25 N + Normal Normal 20.2 Normal L borderline delay
L 0.1 (6/60) −2.25 −1.0 30 −2.75 18.3
IV‐17 IVA M 29.4 R 0.5 (6/12) ‐ ‐ ‐ ‐ N + Normal Normal 22 Normal ‐
L 0.5 (6/12) 21

Notes. MPS, mucopolysaccharidosis; IOP, intraocular pressure; VEP, visual evoked potential; F, female; M, male; R, right; L, left; ‐, not assessed; Y, yes; N, no; +, mild corneal clouding; ++, moderate corneal clouding.