. 2019 Mar 8;7(5):e00617. doi: 10.1002/mgg3.617

Table 5.

The demographic data and ophthalmologic characteristics of seven Taiwanese patients with MPS VI

No.	MPS type	Gender	Age (years)	Right eye or left eye	Visual acuity	Sphere	Cylinder	Axis of cylinder	Refraction (spherical equivalent)	Amblyopia	Corneal opacity	Lens opacity	Optic disc	IOP (mmHg)	Retinal appearance	VEP
VI‐1	VI	M	8.3	R	1.0 (6/6)	+5.0	+1.5	99	+5.75	N	+	clear	Normal	26.3	Normal	Bilateral mild delay
VI‐1	VI	M	8.3	L	0.8 (6/7.5)	+4.75	+2.0	81	+5.75	N	+	clear	Normal	18.7	Normal	Bilateral mild delay
VI‐2	VI	M	8.5	R	1.0 (6/6)	+2.25	+0.5	110	+2.50	N	+	normal	Mild swelling	18.4	Myelinated nerve fiber	Bilateral delay
VI‐2	VI	M	8.5	L	1.2 (6/5)	+1.5	+1.5	75	+2.25	N	+	normal	Normal	14.8	Normal	Bilateral delay
VI‐3	VI	M	9.0	R	0.01 (6/600)	+0.75	+1.0	95	+1.25	Y	+++	‐	‐	35	Poor view	Bilateral delay
VI‐3	VI	M	9.0	L	0.02 (6/300)	+2.25	−2.25	175	+1.13	Y	+++	‐	‐	37	Poor view	Bilateral delay
VI‐4	VI	F	11.7	R	0.2 (6/30)	+8.75	+0.5	101	+9.00	Y	++	clear	Swelling	17.7	Increased vessels tortuosity, vitrous opacities	Bilateral delay
VI‐4	VI	F	11.7	L	0.1 (6/60)	+8.5	+0.75	64	+8.88	Y	++	clear	Swelling	19.5	Increased vessels tortuosity, vitrous opacities	Bilateral delay
VI‐5	VI	F	13.0	R	HM/20 cm	‐	‐	‐	‐	Y	+++	‐	‐	38	Poor view	Bilateral delay
VI‐5	VI	F	13.0	L	HM/5 cm	‐	‐	‐	‐	Y	+++	‐	‐	39	Poor view	Bilateral delay
VI‐6	VI	F	21.4	R	HM/20 cm	‐	‐	‐	‐	Y	+++	‐	‐	25	Poor view	Bilateral delay
VI‐6	VI	F	21.4	L	HM/25 cm	‐	‐	‐	‐	Y	+++	‐	‐	26	Poor view	Bilateral delay
VI‐7	VI	F	25.6	R	0.1 (6/60)	‐	‐	‐	‐	Y	+++	‐	‐	26	Poor view	‐
VI‐7	VI	F	25.6	L	0.15 (6/40)	‐	‐	‐	‐	Y	+++	‐	‐	27	Poor view	‐

Notes. MPS, mucopolysaccharidosis; IOP, intraocular pressure; VEP, visual evoked potential; F, female; M, male; R, right; L, left; HM, hand motion; ‐, not assessed; Y, yes; N, no; +, mild corneal clouding; ++, moderate corneal clouding; +++, severe corneal clouding.