Figure 3. Examination of OXPHOS proteins isolated from patient skin fibroblasts with incompletely assembled mitochondrial CV.

Assessment of mitochondrial OXPHOS proteins in mitochondria isolated from patients with mitochondrial CV deletions and controls, using skin fibroblasts. Results are accompanied by representative immunoblot images with n = 4 per group. Data are presented as mean ± SEM, with * indicating a significant difference between patient and control samples at p < 0.05. CV = complex V; OXPHOS = oxidative phosphorylation.