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. 2019 Jan 22;52(3-4):161–172. doi: 10.1159/000494291

Table 1.

Study characteristics

Study\author, reference number, and year Study design Prevalence year or period Incidence
period
Study region Case ascertainment Included
ages
Included CIDP categories Population
number
Person-years
Lefter et al. [36], 2017 Retrospective and prospective December 31, 2013 NA Republic of Ireland EFNS/PNS 2010 criteria ≥18 years NR 3,439,565 NA

Hafsteinsdottir and Olafsson [32], 2016 NR NA January 1, 1991 – December 31, 2011 Iceland EFNS/PNS 2010 criteria All ages Definite and probable 284,082 5,996,021*

Mahdi-Rogers and Hughes [9], 2014 NR January 1, 2008 NA Southeast
England
EFNS/PNS 2006 criteria NR Definite, probable and possible 3,557,352 NA

Rajabally et al. [18], 2009 NR May 1, 2008 2005–2007 UK,
Leicestershire,
Rutland
EFNS/PNS 2006 criteria, AAN criteria All ages Definite, probable and possible 963,600 2,857,143

Laughlin et al. [33], 2009 NR January 1, 2000 January 1, 1982 – December 31, 2001 USA,
Olmsted County
Dyck et al. [62], 1975 All ages Definite,
probable
NR NR

Iijima et al. [34], 2008 NR September 2004 – August 2005 September 2004 – August 2005 Japan AAN criteria, Saperstein's modified criteria, INCAT, other criteria All ages NA 127,655,000 127,655,000

Ohiò et al. [11], 2007 NR December 31, 2001 1995–2001 Italy,
Piemonte and Valle d'Aosta
AAN criteria All ages Definite, probable and possible 4,334,225 26,005,350*

Mygland and Monstad [10], 2001 Prospective October 31, 1999 NA Norway,
Vest-Agder
Albers and Kelly criteria All ages NA 155,464 NA

McLeod et al. [13], 1999 NR August 6, 1996 1986–1995 Australia,
New South Wales
AAN criteria, Dyck et al. [61], 1993 All ages Definite, probable and possible 5,995,544 58,000,000

Lunn et al. [12], 1999 NR January 1, 1995 NA England,
Four Thames health regions
AAN criteria NR Definite, probable and possible 14,049,850 NA

Kusumi et al. [35], 1995 Retrospective December 31, 1992 NA Japan,
Tottori prefecture
AAN criteria NR NR 614,725* NA

Case definition: Albers and Kelly [60]; AAN criteria, American Academy of Neurology criteria [6]; Dyck et al. [61], 1993; Dyck et al. [62], 1975; EFNS/PNS 2006 criteria [49]; EFNS/PNS 2010 criteria [4]; INCAT, inflammatory neuropathy cause and treatment [5]; Saperstein>s modified criteria [63]; other criteria [64].

Calculated,

*

provided by author of corresponding study. NA, not applicable