Table 3.

Incidence rates

Study author, year, and reference number	Number of cases	Number of male	Number of female	Gender rate ratio cases, male/female	Total incidence per 100,000 population (95% CI)*	Male incidence per 100,000 population (95% CI)*	Female incidence per 100,000 population (95% CI)*	Gender rate ratio incidence, male/ female
Hafsteinsdottir and Olafsson [32], 2016	15#	NR	NR	NR	0.25# 0.3 (0.04–2.47)***	NR	NR	NR
Rajabally et al. [18], 2009 EFNS/PNS 2006 criteria AAN criteria	20 10†	13 NR	7 NR	1.9† NR	0.70 (0.43–1.08) 0.35 (0.17–0.64)	0.92 (0.49–1.58) 0.56 (0.24–1.10)	0.48 (0.19–0.99) 0.14 (0.02–0.50)	1.9† 4.0†
Laughlin et al. [33], 2009	NR	NR	NR	NR	1.4 (0.8–2.0)!,***1.6 (0.9–2.2)***	NR	NR	NR
Iijima et al. [34], 2008	601	354	247	1.4+	0.48	0.58	0.38	1.5†
Ohio et al. [11], 2007	95	NR	NR	NR	0.36 (0.29–0.44) 0.34 (0.28–0.42)**	0.51 (0.39–0.65)	0.22 (0.15–0.31)	2.3†
McLeod et al. [13], 1999	87	NR	NR	NR	0.15	NR	NR	NR

^†Calculated;

^*crude rate, if not specified otherwise;

^**standardized rate;

^***age- and sex-adjusted rate;

^!excluding MGUS;

^#provided by author of corresponding study. NR, not reported; AAN, American Academy of Neurology [6]; EFNS/PNS criteria 2006 [49].