Table 3.

Comparison of ARPKD kidney transplant recipients vs. those without kidney transplant: clinical and demographic characteristics, and liver and spleen shear wave speeds measured by ARFI US elastography.

Characteristic	ARPKD kidney transplant recipients (n = 5)	ARPKD without kidney transplant (n = 20)	P
Age, years	6.1 [4.5, 18.7]	4.3 [0.9, 12.0]	0.2
eGFR*  (mL/min/1.73m2)	65.2 [53.7, 82.4]	62.7 [34.7, 102.7]	0.9
WBC count  (×103/μL)	7.5 [6.3, 7.6]	6.1 [4.3, 11.6]	0.9
Platelets
Count (×103/μL)	199 [147, 241]	271 [90, 355]	0.5
<150×103/μL	2 (40%)	7 (35%)	0.9
Spleen length
Index (actual/90ft percentile)	1.17 [1.11, 1.42]	0.94 [0.88, 1.41]	0.2
>90th percentile	5 (100%)	9 (45%)	0.05
Definite pHTN	2 (40%)	7 (35%)	0.2
SWS (m/s)
Liver left lobe	2.32 [1.87, 2.80]	1.99 [1.73, 3.16]	0.9
Liver right lobe	1.88 [1.69, 2.25]	1.99 [1.58, 2.54]	0.5
Spleen	3.27 [2.97, 3.37]	3.13 [2.86, 3.55]	0.9

Continuous variables given as median [IQR]; binary variables as count (%).

ARPKD, autosomal recessive polycystic kidney disease; eGFR, estimated glomerular filtration rate; pHTN, portal hypertension (Definite pHTN = splenomegaly + low platelets); SWS, shear wave speed; WBC, white blood cell count