Table 1.

Clinical areas of focus and recommended speciality focus

Table	Recommended speciality focus
Table 2: General principles for the management of patients with MPS VI	all
Table 3: Recommended routine monitoring and assessments in patients with MPS VI	all
Table 4: Guidance statement for galsulfase	geneticist, metabolic physician, paediatrician, nurse, physiotherapist
Table 5: Guidance statements for HSCT	anaesthetist, bone marrow transplant expert/hematopoietic stem cell transplant expert, geneticist, paediatrician, nurse
Table 6: Guidance statements for continuous positive airway pressure (CPAP), non-invasive positive pressure ventilation (NIPPV), oxygen supplementation and hypercapnia monitoring	anaesthetist, ear-nose-throat specialist, geneticist, paediatrician, respiratory physician/pulmonologist, nurse
Table 7: Guidance statements for anaesthesia	all
Table 8: Guidance statements for hip reconstruction, hip replacement and growth modulation surgeries	anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 9: Guidance statements for decompression of the spinal cord, spinal stabilisation and thoracolumbar kyphoscoliosis	anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 10: Guidance statement for corneal transplantation	anaesthetist, geneticist, ophthalmologist, paediatrician
Table 11. Guidance statements for decompression of the median nerve, tenosynovectomy and pulley release	anaesthetist, geneticist, hand surgeon, orthopaedic surgeon, neurosurgeon, paediatrician
Table 12: Guidance statement for cardiac valve replacement and left ventricular apical aneurysms	anaesthetist, cardiologist, geneticist, paediatrician
Table 13: Guidance statements for tonsillectomy and/or adenoidectomy, tracheostomy and insertion of ventilation tubes	anaesthetist, geneticist, ear-nose-throat specialist, paediatrician, respiratory physician/pulmonologist