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. 2019 May 31;12:54. doi: 10.1186/s13045-019-0738-1

Table 2.

The relationship between ICB and dMMR/MSI-H

Author/year Cancer type N Protocol Results PFS OS

Le DT [65]

2015

dMMR CRC 41 Pembrolizumab 10 mg/kg, q14d, 20 weeks ORR 40% 20-week PFS, 78%; mPFS: NR mOS: NR
pMMR CRC ORR 0% 20-week PFS, 11%; mPFS: 2.2 months mOS, 5.0 months
dMMR non-CRC ORR 71% 20-week PFS, 67%; mPFS: 5.4 months mOS: NR
pMMR CRC 25

ORR 0%

DCR16%

mPFS, 2.4 months mOS, 6 months

Le DT [30]

2017

12 tumors with dMMR 86 Pembrolizumab 10 mg/kg, q14d, 2 years

ORR 53%

DCR 66%

12-month PFS, 64%

24-month PFS, 53%;mPFS: NR

12-month OS, 76%

24-month OS, 64%;mOS: NR

Diaz LA [66]

2017

Multiple types of solid tumors 77 Pembrolizumab 200 mg, q3w, 35 cycles

ORR 38%

DCR 58%

6-month PFS, 45%

mPFS, 4.3 months

6-month OS, 73%;mOS: NR

D Le [67]

2018

MMR/dMMR CRC 63 Pembrolizumab 200 mg, q3w, 35 cycles

ORR 28%

DCR 51%

6-month PFS, 43%

12-month PFS, 41%;mPFS, 4.1 months

6-month OS, 87%

12-month OS, 76%;mOS: NR

Overman MJ [68]

2017

dMMR/MSI-H mCRC 74 Nivolumab 3 mg/kg, q2w, until PD

ORR 31%

DCR 69% (≥ 12 weeks)

12-month PFS, 50%

mPFS, 14.3 months

12-month OS, 73%;mOS: NR

Overman MJ [71]

2018

dMMR/MSI-H mCRC 119 Nivolumab 3 mg/kg + ipilimumab 1 mg/kg, q3w, 4 doses, followed by nivolumab 3 mg/kg, q2w, until PD

ORR 55%

DCR 80%

9-month PFS, 76%

12-month PFS, 71%;mPFS: NR

9-month OS, 87%

12-month OS, 85%;mOS: NR

H-J J Lenz [72]

2018

dMMR/MSI-H mCRC 45 Nivolumab 3 mg/kg, q2w + ipilimumab 1 mg/kg, q6w, until PD (as first-line treatment)

ORR 60%

DCR 84%

12-month PFS, 78%;mPFS: NR 12-month OS: 83%;mOS: NR

M Chalabi [73]

2018

dMMR early-stage CC

pMMR early-stage CC

7

8

Nivolumab 3 mg/kg, d1, d15 + ipilimumab 1 mg/kg, d1

mPR 100%

mPR 0%

NA NA

Abbreviations: dMMR mismatch repair deficient, CRC colorectal cancer, mCRC metastatic colorectal cancer, CC colon cancers, pMMR mismatch repair proficient, ORR objective response rate, PFS progression-free survival, mPFS median progression-free survival, NR not reached (the responses were durable and the results were not reached until the end of follow-up), mOS median overall survival, DCR disease control rate, OS overall survival, mCRC metastatic colorectal cancer, MSI-H microsatellite instability-high, PD disease progression, mPR major pathological response, NA not available