. Author manuscript; available in PMC: 2020 May 1.

Published in final edited form as: J Cyst Fibros. 2019 Mar 27;18(3):321–333. doi: 10.1016/j.jcf.2019.03.002

Table 5:

Committee’s consensus for testing recommendations for individuals with FEV₁ <40% (adults) or FEV₁ <50% (pediatrics)

Test	Action
6-minute walk test	Annual evaluation
	Refer if distance <400 meters (1,312 feet)
	Refer in the presence of rest or exertional supplemental oxygen requirement
Venous blood gas	Annual evaluation
	Perform arterial blood gas if venous pCO₂ >56 mmHg
	Refer if arterial pCO₂ >50 mmHg
Echocardiogram	Assess baseline estimate of pulmonary pressure
Echocardiogram	Refer if PA systolic pressure >50 mmHg or evidence of right ventricular dysfunction in the absence of a tricuspid regurgitant jet