Table 1.
Electrocardiogram parameters at baseline and after ajmaline administration, results of electrophysiological study and genetic testing.
| Baseline | Ajmaline | EPS | SCN5A variant | |||||||
|---|---|---|---|---|---|---|---|---|---|---|
| HR (bpm) | PR (ms) | QRS (ms) | QTc (ms) | HR (bpm) | PR (ms) | QRS (ms) | QTc (ms) | |||
| II-7 | 68 | 290 | 95 | 410 | 72 | 365 | 138 | 510 | Positive | Yes |
| III-2 | 63 | 186 | 85 | 365 | 69 | 234 | 111 | 401 | Negative | No |
| III-3 | 88 | 220 | 110 | 420 | – | – | – | – | Negative | Yes |
| III-4 | 67 | 170 | 107 | 402 | 85 | 222 | 120 | 450 | Negative | No |
| III-5 | 44 | 181 | 106 | 390 | 59 | 250 | 125 | 445 | Negative | Yes |
| III-6 | 69 | 244 | 103 | 430 | 75 | 330 | 122 | 485 | Negative | Yes |