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. Author manuscript; available in PMC: 2019 Jun 5.
Published in final edited form as: J Inherit Metab Dis. 2015 May 30;39(1):115–124. doi: 10.1007/s10545-015-9860-6

Table 1. tHcy, homocystine and Met concentrations at diagnosis and under treatment.

Parameter units and reference ranges At diagnosis Under treatment
Median (range) Mean n Median (range) Mean n
Plasma tHcy
(5-15 µmol/L)
170
(30-316)
163 28 71(23-127) 73 29
Free homocystine
(µmol/L)
Normally undetectable
29
(9-70)
32 14 3.1(0.6-14) 5.7 8
Urine homocystine
(µmol/ mmol creatinine)
Normally undetectable)
29
(4-627)
113 13 - - 3
Plasma methionine
(10-39 µmol/L)
9
(0-29)
9 30 27 (11-89) 35 23