Table 2.

Intraocular Medulloepithelioma: Clinical features

Symptoms

Leucocoria (20%)

Loss of vision (27%)

Painful red eye (20%)

Asymptomatic (17%)

Strabismus (12%)

Signs

Grey-white Ciliary body mass with cysts

Lens

Loss of zonules and Subluxation (27%)

Notch or coloboma (20%)

Cataract (46%) - Sectoral or Total

Iris

Localised bowing/bulge

Neovascularisation (51%)

Corectopia (29%)

Ectropion uveae (29%)

Retrolental Neoplastic cyclitic membrane (51%)

Secondary glaucoma (44%)

Neovascular glaucoma (83%)

Angle closure glaucoma (17%)

Vitreous haemorrhage (5%)

Retinal detachment (22%)

Extra ocular tumor extension (10%)

Data adapted from[17] Kaliki S., Shields C.L., Eagle Jr. R.C et al. Ciliary body medulloepithelioma: Analysis of 41 cases. Ophthalmology 2013, 120, pp. 2552-2559