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. 2019 May 25;20(10):2573. doi: 10.3390/ijms20102573
ALS amyotrophic lateral sclerosis
ALSFRS-R revised ALS functional rating scale
ANG angiogenin
ANOVA analysis of variance
ATXN2 ataxin 2
C9orf72 chromosome 9 open reading frame 72
CCNF G2/mitotic-specific cyclin F
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
CHMP2B charged multivesicular body protein 2B
DAO D-amino acid oxidase
DCTN1 dynactin-1
DNA deoxyribonucleic acid
EDDs electron dense deposits
ELP3 elongator complex protein 3
ERBB4 transmembrane tyrosine kinase receptor
EWSR1 Ewing sarcoma break point region 1
FIG4 phosphoinositide 5 phosphatase
FUS fused in sarcoma
GATK genome analysis tool kit
GFAP glial fibrillary acidic protein
GLE1 nucleoporin GLE 1 protein
GRN granulin
HNRNPA1 heterogeneous nuclear ribonucleoprotein A1
IBA-1 ionized calcium-binding adapter molecule 1
IgG immunoglobulin G
ip intraperitoneal
MATR3 Matrin 3
MCP-1 macrophage chemoattractant protein 1
NEFH neurofilament heavy
NEK1 never in mitosis gene a related kinase 1
NGS next generation sequencing
OPTN optineurin
PBS phosphate buffered saline
PFN1 profilin 1
s.e.m. standard error of means
s.d. standard deviation
SETX senataxin
SIGMAR1 sigma-non-opioid intracellular receptor 1
SOD1 superoxide dismutase 1
SPG11 spataxin 11
SQSTM1 sequestosome 1
SS18L1 NBAF chromatin remodeling complex subunit
TAF15 TATA-Box binding protein associated Factor 15
TARDBP transactive response DNA-binding protein
TBK1 TANK binding kinase 1 / NF-Kappa-B-activating kinase
TNF-α tumor necrosis factor alpha
TUBA4A tubulin α 4A
UBQLN2 ubiquilin 2
UPS ubiquitin-proteasome system
VAPB vesicle-associated membrane protein
VCP valosin containing protein