| 6-OHDA | 6-hydroxydopamine |
| acetyl-CoA | Acetyl form of coenzyme A |
| ADOA | Autosomal dominant optic atrophy |
| Cas9 | CRISPR-associated protein 9 |
| CMT2 | Charcot-Marie-Tooth Type 2 |
| CNS | Central nervous system |
| COA | COX assembly factor |
| CoQ | Coenzyme Q |
| COX | Cytochrome c oxidase |
| CRISPR | Clustered regularly interspaced short palindromic repeats |
| Cys | Cysteine |
| cyt c | cytochrome c |
| DNP | 2-4 dinitrophenol |
| DOA | Dominant optic atrophy |
| DS | Dravet syndrome |
| EC | Enzyme complexes |
| ENU | N-ethyl-N-nitrosourea |
| Hcy | Homocysteine |
| MADD | Multiple acyl-CoA dehydrogenase deficiency |
| MCS | Mitochondrial carriers |
| MO | Morpholino oligonucleotide |
| MPP+ | 1-methyl-4-phenylpyridinium |
| MPTP | 1-methylmethyl-4-phenylphenyl-1,2,3,6-tetrahydropyridinetetrahydropyridine |
| mRNA | Messenger RNA |
| mtDNA | Mitochondrial DNA |
| nDNA | Nuclear DNA |
| NGS | Next-generation sequencing |
| OxPhos | Oxidative phosphorylation |
| PBA | 4-phenylbutyrate |
| PCH | Pontocerebellar hypoplasia |
| PD | Parkinson’s disease |
| PDHC | Pyruvate dehydrogenase complex |
| pLL | Posterior lateral line |
| PNS | Peripheral nervous system |
| ROS | Reactive oxygen species |
| rRNA | Ribosomal RNA |
| TALEN | Transcription activator-like effector |
| tRNA | Transfer RNA |