| ALS | Amyotrophic Lateral Sclerosis |
| ATM | Ataxia Telangiectasia Mutated |
| ATR | ATM and Rad3-related |
| Chk1 | Checkpoint Kinase 1 |
| Chk2 | Checkpoint Kinase 2 |
| DDR | DNA Damage Repair |
| DSB | Double Strand Break |
| fALS | familial Amyotrophic Lateral Sclerosis |
| FUS | Fused in Sarcoma |
| NES | Nuclear Export Signal |
| NLS | Nuclear Localization Signal |
| PBMC | Peripheral Blood Mononuclear Cell |
| PBS | Phosphate Buffered Saline |
| pSer | phosphoSerine |
| pThr | phosphoThreonine |
| RBP | RNA Binding Protein |
| sALS | sporadic Amyotrophic Lateral Sclerosis |
| Ser | Serine |
| SOD1 | Superoxide dismutase 1 |
| SSB | Single Strand Break |
| TARDBP | TAR DNA Binding Protein |
| Thr | Threonine |