Table 1.

Clinical and demographic characteristics

	Neurology clinic n=54	Multidisciplinary care clinic n=344	p-value
Age at onset in years (range)	58 (30–77)	62 (24–87)	0.01
Gender	M: 35 (64.8%)	M: 183 (53.6%)	0.14
Type of onset
Spinal	41 (75.9%)	229 (66.65%)	0.35
Bulbar	11 (20.4%)	103 (29.9%)
Respiratory	2 (3.7%)	12 (3.5%)
Riluzole	16 (29.6%)	305 (88.7%)	<0.001
NIMV	7 (13%)	168 (48.8%)	<0.001
Gastrostomy	2 (3.7%)	111 (32.3%)	<0.001
Family history	2 (3.2%)	4 (1.1%)	0.20
Time to NIMV (months)	25	14	<0.001
Diagnostic delay (months)	8	10	0.15

Abbreviation: NIMV, noninvasive mechanical ventilation.