Table 2.
Outcome data from case reports on KD in GSDIII for: author, patient number, age, length of follow-up, heart function and liver function effect, side effects.
| Study | No. patients/age | Diet | Follow-up | Heart function | Liver function | Side effects |
|---|---|---|---|---|---|---|
| Valayannopoulos V 6 (2011) | 1
(2 mo) |
2:1 KD plus 3OHB | 24 months | Improved | Stable | None |
| Brambilla A 5
(2014) |
2
(5,7 y) |
High-fat high-protein low-CHO | 12 months | Improved | Improved | None |
| Mayorandan S 18
(2014) |
2
(9,11 y) |
MAD | 32-26 months | Improved | Not reported | Transient asymptomatic hypoglycemia |
| Francini F | 1
(34 y) |
MAD | 12 months | Improved | Improved | Increase of uric acid plasma level and C-LDL |