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. 2019 Jun 9;3(2):ytz095. doi: 10.1093/ehjcr/ytz095

Table 1.

Clinical characteristics of patients with type 1 myotonic dystrophy presenting with ventricular tachycardia

Patient Age (years)/ gender HR (b.p.m.) ECG findings (ms) Echocardiographic parameters VT detection Presentation Medications
1 44/F 82

  • PR: 212; QRS: 105 QTc: 476

  • Biventricular paced rhythm

  • LVEF: 46%

  • LVMI: 56.6 g/m2

  • LVIDd: 5.0 cm

  • LVIDs: 4.3 cm

 CRT-P Cardiac Arrest

  • Mexiletine

  • Perindopril
2 36/F 69

  • PR: 179; QRS: 146 QTc: 388

  • Atrial-paced rhythm, LBBB

  • LVEF: 46%

  • LVMI: 60.9 g/m2

  • LVIDd: 4.6 cm

  • LVIDs: 3.7 cm

 DC-PPM Asymptomatic

  • Furosemide

  • Ramipril

  • Spironolactone
3 49/M 86

  • PR: 200; QRS: 107 QTc: 442

  • LAFB

  • LVEF: 45%

  • LVMI: 51.5 g/m2

  • LVIDd: 4.0 cm

  • LVIDs: 3.3 cm

 Tele-monitoring Syncope

  • ASA

  • Metoprolol

  • Ramipril

  • Rosuvastatin
4 61/M 64

  • PR: 272; QRS: 168 QTc: 446

  • Atrial-paced rhythm, LBBB

  • LVEF: 45%

  • LVMI: 69.7 g/m2

  • LVIDd: 4.8cm

  • LVIDs: 2.5cm

 DC-PPM Palpitations

  • Atorvastatin

  • Candesartan

  • Spironolactone
5 40/M 71

  • QRS: 170; QTc: 474

  • Atrial fibrillation, biventricular paced rhythm

  • LVEF: 38%

  • LVMI: 137 g/m2

  • LVIDd: 6.6cm

  • LVIDs: 5.1cm

 CRT-D ICD shock

  • Digoxin

  • Ramipril

  • Warfarin

Refer to Methods section for how values were obtained or calculated.

ASA, acetylsalicylic acid; CRT-D, cardiac resynchronization therapy defibrillator; CRT-P, cardiac resynchronization therapy pacemaker; DC-PPM, dual-chamber permanent pacemaker; ECG, electrocardiogram; LBBB, left bundle branch block; LV, left ventricle; LVEF, left ventricular ejection fraction; LVIDd, left ventricle internal diameter end diastole; LVIDs, left ventricle internal diameter end systole; VT, ventricular tachycardia.