Table 2.
Total prevalence of CCHD types per 10 000 births, International Clearinghouse for Birth Defects Surveillance and Research (ICBDSR) Critical Congenital Heart Defects (CCHD) Prenatal Diagnosis study 2000–2014*
| Programme (by geographic region) |
HLHS | COA | AoS | TOF | DTGA | DORV | PTA | IAA | PulmA | TriA/HRH | SV | TAPVR | Total prevalence |
| UK-Wales | 3.3 | 5.0 | 2.5 | 3.5 | 3.4 | 1.3 | 1.1 | 0.8 | 1.3 | 0.5 | 0.9 | 1.1 | 24.7 |
| Germany-Saxony Anhalt | 2.7 | 4.5 | 1.3 | 3.3 | 3.3 | 0.7 | 0.6 | 0.2 | 0.9 | 0.3 | 0.4 | 0.6 | 18.8 |
| Netherlands-Northern | 3.3 | 3.6 | 2.2 | 3.3 | 3.7 | 1.1 | 0.4 | 0.4 | 1.3 | 0.4 | 0.9 | 0.7 | 21.4 |
| France-Rhone Alpes | 4.6 | 2.2 | 0.8 | 3.5 | 4.0 | 1.0 | 0.8 | 0.1 | 0.8 | 0.9 | 1.1 | 0.2 | 20.0 |
| Italy-Lombardy | 3.2 | 4.9 | 1.1 | 4.9 | 1.4 | 1.4 | 0.4 | 0.0 | 0.7 | 0.7 | 0.7 | 0.0 | 19.3 |
| Italy-Emilia Romagna | 2.6 | 3.1 | 0.6 | 3.8 | 2.9 | 1.2 | 0.7 | 0.2 | 0.8 | 0.8 | 0.8 | 0.4 | 17.9 |
| Italy-Tuscany | 2.3 | 2.0 | 0.5 | 2.5 | 2.7 | 0.8 | 0.3 | 0.1 | 0.5 | 0.4 | 0.5 | 0.2 | 12.7 |
| Malta | 4.1 | 4.1 | 1.2 | 3.3 | 4.7 | 0.6 | 0.4 | 0.4 | 1.2 | 0.8 | 1.6 | 0.2 | 22.9 |
| Czech Republic | 3.3 | 5.7 | 4.9 | 3.8 | 3.6 | 3.4 | 1.3 | 0.8 | 1.8 | 0.6 | 0.9 | 0.8 | 30.9 |
| Slovak Republic | 2.3 | 1.2 | 0.8 | 1.8 | 1.0 | 0.7 | 0.9 | 0.2 | 0.5 | 0.3 | 0.4 | 0.2 | 10.3 |
| Canada | 1.9 | 4.9 | 1.5 | 3.9 | 3.0 | 1.2 | 0.5 | 0.1 | 0.8 | 0.5 | 0.4 | 1.0 | 19.5 |
| USA-Arkansas | 3.2 | 4.7 | 2.0 | 0.9 | 2.4 | 1.1 | 0.6 | 0.5 | 0.7 | 0.5 | 0.8 | 1.0 | 18.3 |
| USA-Atlanta | 2.2 | 4.0 | 1.1 | 4.8 | 2.0 | 0.5 | 0.8 | 0.3 | 0.6 | 0.6 | 0.9 | 0.7 | 18.7 |
| Argentina | 1.9 | 1.5 | 0.3 | 1.5 | 1.5 | 0.5 | 0.4 | 0.3 | 0.3 | 0.2 | 1.1 | 0.5 | 10.1 |
*ICBDSR programmes contributed data for different years within this time period (see table 1).
AoS, aortic valve stenosis; CCHD, critical congenital heart defects; COA, coarctation of the aorta; DTGA, d-transposition of great arteries; DORV, double outlet right ventricle; HLHS, hypoplastic left heart syndrome; IAA, interrupted aortic arch; PulmA, pulmonary valve atresia with intact ventricular septum; PTA, persistent truncus arteriosus; SV, single ventricle; TOF, tetralogy of Fallot; TriA/HRH, tricuspid valve atresia/hypoplastic right heart; TAPVR, total anomalous pulmonary venous return.