Table 1.
No. | Mutation | CC | AC | HC | Septum pellucidum | CP | Cerebellum |
---|---|---|---|---|---|---|---|
1 | SMARCB1 c.1121G>A p.(Arg374Gln) | Short stubby | Not visible | Not visible | Present | Normal | Normal |
8 | SMARCB1 c.1121G>A p.(Arg374Gln) | Short stubby | Not visible | Not visible | Present | Normal | Normal |
9 | SMARCB1 c.1091_1093delAGA p.(Lys364del) | Short | Normal | Normal | Present | Normal | Large posterior fossa, hypoplastic vermis, cerebellar hypoplasia |
10 | SMARCB1 c.1091_1093delAGA p.(Lys364del) | Short thin | Small | Small | Normal | Normal | Enlarged fourth ventricle, mild vermis hypoplasia |
11 | SMARCB1 c.1121G>A p.(Arg374Gln) | Short thin | Normal | Normal | Normal | Normal | Normal |
2 | ARID1B c.5961_5964delGAGA p.(Arg1988Serfs*32) | Normal | Normal | Normal | Present | Normal | Normal |
3 | ARID1B c.3604_3610dupTCCATGG p.(Ala1204Valfs*8) | Short stubby | Small | Small | Present | Normal | Normal |
4 | ARID1B c.5346dupT p.(Lys1783*) | Absent | Absent | Absent | Absent | Voluminous | Normal |
5 | ARID1B c.2191_2192dupAT p.(Pro732Serfs*14) | Normal | Normal | Normal | Present | Normal | Normal |
6 | ARID1B c.5910_5928del p.(Pro1973Argfs*29) | Absent | Small | Small | Absent | Normal | Normal |
7 | SMARCE1 c.218A>C p.(Tyr73Ser) | Short thin | Small | Small | Hypoplastic | Normal | Large posterior fossa, vermis hypoplasia, cerebellar dysplasia |
Abnormalities are highlighted in bold
No. patient number, CC corpus callosum, AC anterior commissure, HC hippocampal commissure, CP choroid plexus, CSS Coffin–Siris syndrome, MRI magnetic resonance imaging