Fig. 4. Disease severity according to the types of initial symptoms. A: The onset age was significantly younger in the subgroup with limb-girdle phenotype. B: The duration from the onset to the diagnosis was significantly longer in the subgroup with limb-girdle phenotype. C and D: Disease progression as represented by the functional joint sets according to disease duration did not differ between the subgroups of foot-drop onset and limb-girdle phenotype (p=0.5731).