Table 1.

Baseline Characteristics of the NHLBI LAM Registry Cohort (N = 217)

Characteristic	Mean ± SD or No. (%)
Age at initial registry visit, y	44 ± 10
Age at disease diagnosis, y	41 ± 10
VEGF-D, pg/mL	1,572 ± 1,696
CT score	11 ± 5
No. of patients with sporadic LAM	180 (83)
No. of patients with TSC-LAM	36 (17)
No. of postmenopausal patients	135 (62)
No. of patients with renal AML(s)	88 (41)
No. of patients with at least one spontaneous pneumothorax	120 (55)
No. of patients with a bronchodilator response	48 (22)
No. of patients with supplemental oxygen use	70 (32)

AML = angiomyolipoma; LAM = lymphangioleiomyomatosis; NHLBI = National Heart, Lung, and Blood Institute; TSC = tuberous sclerosis complex; VEGF-D = vascular endothelial growth factor-D.