Table 2.

Autoimmune manifestations in 134 patients with CID-G/AI or with AS

Manifestation	CID-G/AI (n = 68) N (%)	AS (n = 66) N (%)
Cytopenias	36 (53)	38 (57.6)
AIHA	25 (36.7)	33 (50)
ITP	17 (25)	11 (16.6)
AIN	15 (22.1)	8 (12.2)
IBD, enteropathy	9 (13.2)	–
Vitiligo	8 (11.7)	–
Hypo/hyper-thyrodism	7 (10.3)	1 (1.5)
Vasculitis	6 (8.8)	3 (4.5)
Alopecia	5 (7.4)	1 (1.5)
Liver disease	4 (5.9)	1 (1.5)
Autoimmune neuropathies	4 (5.9)	–
Autoimmune myopathies	4 (5.9)	–
Nephritis	3 (4.4)	1 (1.5)

AIHA, autoimmune hemolytic anemia; AIN, autoimmune neutropenia; AS, atypical SCID; CID-G/AI, combined immune deficiency with granuloma and/or autoimmunity; IBD, inflammatory bowel disease; ITP, immune thrombocytopenia