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. 2019 Jul 19;10:1272. doi: 10.3389/fimmu.2019.01272

Table 1.

Age range and median age at last news from patient in years of the 12 most prevalent PID diagnoses and WAS, XLP, and FHLH (patients with no HSCT or gene therapy), living patients.

12 PIDs, WAS, XLP, FHLH Male (n) Female (n) Total (no HSCT/no gene therapy) Age range (years) Median age (years) Living patients with and withoutHSCT/gene therapy
CVID 313 352 665 99.8% 3–88 40 666
Unclassified antibody deficiency 102 119 221 99.1% 0–80 28 223
CGD 46 12 58 51% 0–59 21 114
Agammaglobulinemia 90 7 97 98% 2–54 17 99
Isolated IgG subclass deficiency 40 42 82 100% 4–68 39 82
SCID 6 2 8 11% 0–21 15 76
Unclassified IDs 22 20 42 93% 3–79 20 45
Combined ID 21 17 38 60% 3–57 18 63
DGS 25 27 52 100% 0–40 8 52
Selective IgA deficiency 17 30 47 100% 3–75 23 47
A-T 30 25 55 96% 3–37 13 57
HIES 28 19 47 85% 0–43 16 55
WAS 7 0 7 25% 0–31 20 28
XLP 14 1 15 68% 7–52 19 22
FHLH 3 0 3 17% 2–13 7 18
Total 763 672 1,437 87% 0–88 1,647