Figure 1.

Ideogram showing current terms that describe different arrhythmogenic cardiomyopathy phenotypes and their possible relationship to left (LV) and right ventricular (RV) disease. By definition, arrhythmogenic RV cardiomyopathy affects predominantly the right ventricle but biventricular forms are frequently seen. Arrhythmogenic dilated cardiomyopathy and left-dominant arrhythmogenic cardiomyopathy describe overlapping entities that mostly affect the left ventricle but RV involvement is also observed. Isolated non-ischaemic scar and hypokinetic non-dilated cardiomyopathy mostly refer to predominantly LV scarring identified using cardiac magnetic resonance imaging.^1–3