| ALP | autophagy-lysosomal pathway |
| ALS | Amyotrophic lateral sclerosis |
| CGP | CGP-37157 |
| CNQX | 6-cyano-7-nitroquinoxaline-2,3-dione |
| CsA | cyclosporine A |
| DMEM | Dulbecco’s Modified Eagle’s Medium |
| FBS | fetal bovine serum |
| FTLD | frontotemporal lobar degeneration |
| GST | glutathione S-transferase |
| MTT | 3-(4,5-dimethylthiazol-2-yl)-2,5-diphenyltetrazolium bromide |
| TDP-43 | TAR DNA-binding protein 43 |
| TDP-43 IBs | TDP-43 inclusion bodies |
| UPS | ubiquitin-proteasome system |