TABLE 1.
Mutually exclusive congenital heart defect categories by ICD-9-CMa codes
| Category | ICD-9-CM code | Code description |
|---|---|---|
| Severe (case has a severe code, regardless of presence of shunt, valve, or other codes) |
745.0 | Common truncus |
| 745.1 | Transposition of the great arteries (TGA) | |
| 745.10 | Complete TGA (dextro-TGA), not otherwise specified (NOS) or classical | |
| 745.11 | Double outlet right ventricle, or incomplete TGA | |
| 745.12 | Corrected TGA (levo-TGA) | |
| 745.19 | TGA, other specified | |
| 745.2 | Tetralogy of Fallot | |
| 745.3 | Single ventricle, or cor triloculare | |
| 745.6 | Endocardial cushion defect | |
| 745.60 | Endocardial cushion defect unspecified | |
| 745.61 | Atrial septal defect (ASD) primum | |
| 745.69 | Endocardial cushion defect, other specified | |
| 746.01 | Pulmonary valve atresia or absence | |
| 746.1 | Tricuspid atresia, stenosis, or absence | |
| 746.7 | Hypoplastic left heart syndrome | |
| 747.11 | Interrupted aortic arch | |
| 747.41 | Total anomalous pulmonary venous return | |
| Shunt + valve (case has shunt AND valve codes) |
A combination of the shunt/valve codes below | A combination of the shunt/valve defects below |
| Shunt (case has at least one shunt code, no valve or severe codes) |
745.4 | Ventricular septal defect (VSD) |
| 745.5 | ASD secundum or patent foramen ovale (PFO) | |
| 745.8 | Other specified defect of septal closure | |
| 745.9 | Unspecified defect of septal closure | |
| 747.0 | Patent ductus arteriosus (PDA) | |
| 747.1/747.10 | Coarctation of aorta | |
| Valve (case has at least one valve code, no shunt or severe codes) |
746.0 | Anomalies of pulmonary valve |
| 746.00 | Pulmonary valve anomaly, unspecified | |
| 746.02 | Pulmonary valve stenosis | |
| 746.09 | Pulmonary valve anomaly, other specified | |
| 746.2 | Ebstein anomaly | |
| 746.3 | Aortic valve stenosis | |
| 746.4b | Aortic insufficiency or bicuspid/unicuspid aortic valveb | |
| 746.5 | Mitral stenosis or mitral valve abnormalities | |
| 746.6b | Mitral insufficiencyb | |
| 747.3b | Anomalies of pulmonary arteryb | |
| 747.31 | Pulmonary artery atresia, coarctation, or hypoplasia | |
| 747.39 | Anomalies of pulmonary artery, other specified | |
| Other only (case only has one or more codes in this category) |
745.7 | Cor biloculare |
| 746.8 | Other specified anomalies of heart | |
| 746.81 | Subaortic stenosis | |
| 746.82 | Cor triatriatum | |
| 746.83 | Infundibular or subvalvar pulmonary stenosis | |
| 746.84 | Obstructive anomalies of heart | |
| 746.85 | Coronary artery anomaly | |
| 746.87 | Malposition of heart or apex | |
| 746.89b | Other specified anomaly of heart (various types)b | |
| 746.9b | Unspecified defect of heartb | |
| 747.2 | Other anomalies of the aorta | |
| 747.20 | Anomalies of aorta, unspecified | |
| 747.21 | Anomaly of aortic arch | |
| 747.22 | Atresia or stenosis of aorta | |
| 747.29 | Other anomalies of aorta, other specified | |
| 747.4 | Anomalies of great veins | |
| 747.40b | Anomalies of great veins, unspecifiedb | |
| 747.42 | Partial anomalous venous return | |
| 747.49 | Other anomalies of great veins | |
| 747.9b | Unspecified anomalies of circulatory systemb |
a
International Classification of Disease, Ninth Revision, Clinical Modification.
b
Codes considered to be minor. All other listed codes considered to be major.