Table 3.
Characteristics of PHEO and Paraganglioma in Patients Younger Than Age 19 Years With VHL Disease
| Family/Case No. | Age at Diagnosis (y) | Sex (F/M) | PHEOa (cm) (Right or Left Side) | Bilateral (Y/N) | Synchronous (Y/N) | Contralateral PHEOa (cm) (Right or Left Side) | Paragangliomaa (cm) | Time Until Recurrence (mo) |
|---|---|---|---|---|---|---|---|---|
| 1/2 | 4 | M | 5.0 (R) | Y | N | 4.0 (R), 1.5 (L) | — | 36 |
| 1.3 (L) | 156 | |||||||
| 2/4 | 8 | F | 6.0 (L) | Y | N | 5.5 (R) | — | 24 |
| 4/10 | 12 | M | 5.5 (R) | Y | Y | 1.5 (L) | 2.2 | — |
| 6/13 | 16 | M | 1.7 (R) | N | N | — | — | No recurrence (follow-up, 83 mo) |
| 19/26 | 13 | M | NA | Y | N | NA | — | 48 |
| 19/27 | 10 | M | NA | Y | N | NA | — | 48 |
Abbreviations: —, case did not develop the tumor; NA, not available.
a
Largest diameter.