Age predilection |
Patients are usually between 20 and 70 years of age, with an average age at presentation of 45 years |
Gender |
Female |
Incidence |
Less than 300 cases have been reported and fewer than 100 cases with cardiac involvement
Extra-uterine involvement is seen in 30% to 80% of cases of uterine intravenous leiomyomatosis, with cardiac involvement in 10% to 30%
|
Risk factors |
History of leiomyomatosis, myomectomy or hysterectomy |
Treatment |
Surgical: including a combined multidisciplinary thoraco-abdominal surgical approach |
Prognosis |
Usually benign |
Findings on imaging |
Ultrasound: a floating mass occupying the IVC, right atrium, and right ventricle characterized by intralesional vascularization with a triphasic CDUS waveform
Computed Tomography: heterogeneous enhancing mass directly extending into the IVC; typical “walking stick head” or “snake head” tumor masses are observed when the right heart is also involved
|