Table 1.

Classification of multiple basaloid follicular hamartoma

Type	Features
Inherited
Familial multiple BFH	Inherited as an autosomal dominant disorder characterized by multiple lesions on face, trunk and extremities
Generalized BFH syndrome	Inherited autosomal dominantly due to mutation in PTCH gene. Manifestations include generalized congenital or childhood onsed multiple BFH with multiple milia, comedo-like lesions, hypotrichosis, hypohidrosis, and palmar and/or plantar pits
Congenital
Congenital generalized BFH	Generalized BFH associated with alopecia and cystic fibrosis
Acquired
Linear unilateral BFH	Multiple grouped lesions in a band-like fashion along the lines of Blaschko. This form of BFH has been described with extensive trichoblastoma, Graves’ disease, congenital dorsal scoliosis and Happle-Tinschert syndrome
Generalized BFH with associated anomalies	Acquired generalized BFH may be associated with myasthenia gravis, alopecia and systemic lupus erythmatosus
Generalized BFH without associated anomalies	Multiple acquired BFH rarely occur sporadically

BFH = Basaloid follicular hamartoma