A) Searching for DNMBP:p.Cys1413Trp, MARRVEL’s result page show
that there is no known Gene-Phenotype Relationship curated by OMIM, meaning it
is not associated with a known disease. Furthermore, this variant is commonly
found in the control population database gnomAD. There are 16868 individuals who
are homozygous for this variant, indicating that this variant is most likely
benign.
B) Searching for IRF2BPL, MARRVEL’s result page show that it is
associated with a known autosomal dominant disease called Neurodevelopmental
disorder with regression, abnormal movements, loss of speech, and seizures. In
the Control Population Gene Summary box for gnomAD database, the pLI score is
0.96, o/e score is 0.11 with the upper bound of 0.33. This means that this gene
is highly intolerant of loss-of-function and the loss of one copy of this gene
may lead to haploinsufficiency phenotypes.