Table 3.
Clear cell sarcoma: clinical data
| Patient no. | Age at diagnosis (years) |
Size (cm) |
Primary tumor site surgery (months after diagnosis) |
Radiation treatment | Chemotherapy | Lymph node involvement (months after diagnosis) |
Distant metastases | Status (months) |
|---|---|---|---|---|---|---|---|---|
| 1 | 48 | 4 | Local/leg (0) | Yes | Yes | Yes (6) | Vertebrae, ribs mediastinum | DWD (16) |
| 2 | 38 | 9 | Incomplete/buttock (6)a | No | Yes | Yes (6) | Lungs, brain, colon | DWD (13) |
| 3 | 58 | 5 | Local/forearm (24) | No | No | Yes (72) | No | NED (87) |
| 4 | 58 | 6.5 | Local/wrist (2) | No | No | No nodes, local recurrence (11) | No | NED (50) |
| 5 | 46 | 3 | Local/heel (0) | Yes | Yes | Yes (5) | Lungs | DWD (12) |
| 6 | 15 | 5 | Local/thigh (0) | Yes | Yes | No (91) | No | NED (91) |
| 7 | 60 | 3 | Syme/foot (1) | No | Yes | No (2) | No | DWOD (2) |
| 8 | 29 | 5 | BKA/foot (1) | Yes | Yes | Yes (13), local recurrence | Lungs | DWD (17) |
| 9 | 16 | 2.5 | BKA/heel (0) | No | Yes | Yes (8) | No | NED (68) |
| 10 | 7 | 2 | BKA/ankle (1) | No | Yes | No (19) | No | NED (19) |
| 11 | 36 | 3 | BKA/heel (0) | Yes | Yes | Yes (30) | Lungs | DWD (31) |
Abbreviations: local, local resection of tumor; Syme, Syme amputation (disarticulation of ankle joint); BKA, below-knee amputation; DWD, dead with disease; NED, no evidence of disease; DWOD, dead without disease.
a
Only patient with lymph node involvement at the time of primary tumor site surgery.