TABLE 1.

Participant Characteristics.

Ethnicity	Sex	Pancreatitis Diagnosis Age, y	Pancreatic Function at Pancreatitis Diagnosis		Sweat Cl, mmol/L	No. Pancreatitis Attacks	Imaging		Interventions	Abnormal Chest Imaging (CT, XR)	Mutation
Ethnicity	Sex	Pancreatitis Diagnosis Age, y	Exocrine	Endocrine	Sweat Cl, mmol/L	No. Pancreatitis Attacks	Chronic Features	Presence of PFC	Interventions	Abnormal Chest Imaging (CT, XR)	Mutation
Patients with CF diagnosis based on SCT >60 mmol/L
Hispanic	M	10	PS	Normal	71	2	N	N	None	No imaging	No mutations
White	F	12	PI	Normal	68	1	Y	N	ERCP	No imaging	c.3773dupT, c.5T-TG12
White	M	12	PS	Normal^*	69	>5	N	N	None	CT + CXR	12TG; C.1408A > G (also NOD2 mutation)
Hispanic	M	16	PI	Impaired	65	>5	Y	PFC	ERCP, celiac plexus block, TPLAT	Normal	c,1521_1523del; c.617T>G^†
White	F	16	PI	Normal	104	2	N	PFC	ERCP	CT + CXR	C.178G > T
African American, Asian	M	16	PS	Normal^*	62	4	Y	N	ERCP	Normal	No mutations detected
Hispanic	M	20	PS	Normal	103	6	Y	N	ERCP	Normal	c.1521 1523del; c.2657 + 5G > A^†
White	M	26	PS	Insulin	95	4	N	2 PFC	None	Normal	No mutations
Patients with CF diagnosis with 2 disease-causing mutations and intermediate sweat test (30–59 mmol/L) or no sweat test
Hispanic	F	8	PI	Normal	38	1	Y	WON	ERCP	CT + CXR	c,1521_1523del; 12TG-5T^‡
White	F	13	PI	Normal^*	38	6	Y	2 PFC	ERCP	No imaging	c3140–26A > G; c. [350G > A;1210–12T[7]^†
White	M	14	PS	Impaired^*	52	>10	Y	N	ERCP	Normal	c.1521 1523del; c.3208C > T;7 T/9 T^†
White	M	21	PS	Normal^*	N/A	4	Y	N	ERCP	CT + CXR	c,1521_1523del; c.350G > A^†
White	F	27	PI	Insulin	N/A	>10	N	N	ERCP	CT	c.350G > A; c,1657C>T^†
Patients with CFTR-RD (intermediate sweat test and 0–1 disease-causing mutation)
White	F	9	PS	Normal	47	2	N	N	None	No imaging	c.3162T > A; 5T
Hispanic	F	10	PS	Impaired	57	>10	N	N	ERCP	Normal	(TG)l 1–5T; (TG)l 1–7T
White	F	10	PI	Impaired	57	4	Y	N	ERCP, TPLAT	No imaging	No mutations detected^‡
Hispanic	M	16	PS	Normal	41	1	Y	N	ERCP	No imaging	(TG)l 1–5T
Hispanic	M	17	PI	Impaired^*	43	3	N	2 PFC	None	No imaging	c.601G > A

Oral glucose tolerance test performed.

^†

Accepted for ivacaftor use.

^‡

Positive SPINK1 mutation.

CT indicates computed tomography; CXR, chest x-ray; F, female; M, male; N/A, not available; PI, pancreatic insufficient; PS, pancreatic sufficient; WON, walled-off necrosis.