Table 1.
Demographics (n=1,417)
| Race/ethnicity | N (%) |
|---|---|
| Age at diagnosis (years) | |
| 1st quartile | 0.0 |
| Median | 1.0 |
| Mean | 2.7 |
| 3rd quartile | 4.0 |
| Range | 0 to 18 |
| Sex | |
| Female | 690 (48.7) |
| Male | 727 (51.3) |
| Race | |
| American Indian/Alaska Native | 14 (1.0) |
| Asian | 129 (9.1) |
| Black | 186 (13.1) |
| Native Hawaiian/other Pacific Islander | 10 (0.7) |
| White | 852 (60.1) |
| Multiracial | 23 (1.6) |
| Not specified | 203 (14.3) |
| Ethnicity | |
| Hispanic/Latino | 227 (16.0) |
| Non-Hispanic/Latino | 1056 (74.5) |
| Not specified | 134 (9.5) |
| PH subtypes | |
| PAH | 591 (41.7) |
| Idiopathic | 163 (11.5) |
| Heritable | 26 (1.8) |
| Drugs/toxins | 2 (0.1) |
| Associated PAH | 403 (28.4) |
| Connective tissue disease (CTD) | 7 (0.5) |
| HIV | 0 |
| Portal hypertension | 6 (0.4) |
| Congenital heart disease (CHD) | 390 (27.5) |
| Schistosomiasis | 4 (0.3) |
| PVOD | 9 (0.6) |
| Persistent PH of the newborn (PPHN) | 46 (3.2) |
| Left-heart disease | 49 (3.5) |
| Lung disease | 688 (48.6) |
| CTEPH | 7 (0.5) |
| Unclear mechanisms | 31 (2.2) |
| Hematological | 8 (0.6) |
| Systemic disorders | 7 (0.5) |
| Metabolic disorders | 3 (0.2) |
| Segmental PH | 3 (0.2) |
| Others | 3 (0.2) |
| Neighborhood socioeconomic indicator | |
| Percentage of children living in poverty at the county level | |
| 1st quartile | 8.3 |
| Median | 11.1 |
| Mean | 12.5 |
| 3rd quartile | 15.3 |
| Range | 3.0 to 36.2 |