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. 2019 Feb 8;27(6):888–902. doi: 10.1038/s41431-019-0354-0

Table 2.

Mean (SD) age and selected clinical data for patients in genotype Group A and Group B from SONIA2 study

	Group A	Group B	p-Value
	(G161R/G161R)	(M368V/M368V+A122V/A122V)
	N = 16	N = 17
Age (years)	52.8 (8.74)	41.5 (7.75)	<0.001
s-HGA (µmol/L)	28.3 (8.26)	28.7 (8.62)	0.898
u-HGA₂₄ (mmol)	35.3 (11.9)	32.5 (9.33)	0.466
u-HGA/u-urea (ratio)	124 (22.7)	107 (21.6)	0.037
Eye pigmentation (score)	16.3 (9.29)	13.6 (5.30)	0.327
Area bone density (g/cm²)	0.828 (0.185)	0.910 (0.127)	0.145
Cobbs angle; scoliosis (°)	37.8 (8.55)	40.5 (9.81)	0.406
Peak aortic velocity (m/s)	1.95 (0.787)	1.45 (0.358)	0.024