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. 2019 Jul 17;90(10):1165–1170. doi: 10.1136/jnnp-2018-320288

Table 1.

Baseline demographics and characteristics

Variable Total N=66
Age, years
 Median 56.5
 Range 36–75
Sex, n (%)
 Male 47 (71.2)
 Female 19 (28.8)
Weight, kg
 Mean (SD) 76.7 (15.9)
BMI, kg/m2
 Mean (SD) 25.6 (4.0)
Race, n (%)
 Caucasian 61 (92.4)
 Asian 3 (4.5)
 Black 1 (1.5)
 Other 1 (1.5)
Disease duration from symptom onset, months
 Median 21.2
 Range 12–48
Sitting SVC % of predicted
 Mean (SD) 75.3 (9.1)
Supine SVC % of predicted
 Mean (SD) 73.3 (14.0)
ALSFRS-R
 Mean (SD) 36.7 (5.4)
Site of disease onset, n (%)
 Spinal 55 (83.3)
 Bulbar 11 (16.7)
Treated with riluzole, n (%) 66 (100)

ALSFRS-R, Amyotrophic Lateral Sclerosis Functional Rating Scale-Revised; BMI, body mass index; SVC, slow vital capacity.