Table 1.
Variable | Total N=66 |
Age, years | |
Median | 56.5 |
Range | 36–75 |
Sex, n (%) | |
Male | 47 (71.2) |
Female | 19 (28.8) |
Weight, kg | |
Mean (SD) | 76.7 (15.9) |
BMI, kg/m2 | |
Mean (SD) | 25.6 (4.0) |
Race, n (%) | |
Caucasian | 61 (92.4) |
Asian | 3 (4.5) |
Black | 1 (1.5) |
Other | 1 (1.5) |
Disease duration from symptom onset, months | |
Median | 21.2 |
Range | 12–48 |
Sitting SVC % of predicted | |
Mean (SD) | 75.3 (9.1) |
Supine SVC % of predicted | |
Mean (SD) | 73.3 (14.0) |
ALSFRS-R | |
Mean (SD) | 36.7 (5.4) |
Site of disease onset, n (%) | |
Spinal | 55 (83.3) |
Bulbar | 11 (16.7) |
Treated with riluzole, n (%) | 66 (100) |
ALSFRS-R, Amyotrophic Lateral Sclerosis Functional Rating Scale-Revised; BMI, body mass index; SVC, slow vital capacity.