LRBA disease symptoms display different responses to abatacept treatment. A, The remission rates for immune dysregulation (ID), chronic diarrhea and lymphoproliferation. B, The comparison of the remission rates of hematological ID (autoimmune hemolytic anemia, immune thrombocytopenia) versus other immune dysregulatory symptomatologies (Diabetes, alopecia, arthritis, demyelinating disease, granulomatous-lymphocytic interstitial lung disease). The remissions are indicated as complete (CR), partial (PR) or non-responsive (NR). The bars are presented as percentages. * p<.01, Chi-square test.