Table 1.
Estimated numbers of patients in Japan with idiopathic portal hypertension (IPH), extrahepatic portal hypertension (EHO), and Budd–Chiari syndrome (BCS) in 1999, 2005, and 2015 epidemiologic surveys
| 1999 | 2005 | 2015 | ||
|---|---|---|---|---|
| IPH | No. of total cases (95% CI) | 920 (710–1140) | 850 (640–1070) | 1000 (810–1300) |
| Period prevalence, per million | 7.3 | 6.7 | 7.9 | |
| Proportion of newly diagnosed cases, % | 31 | 21 | 10 | |
| No. of newly diagnosed cases | 290 (220–350) | 180 (130–220) | 100 (80–130) | |
| Period incidence, per million | 2.3 | 1.4 | 0.8 | |
| EHO | No. of total cases (95% CI) | 720 (540–1040) | 450 (340–560) | 770 (610–930) |
| Period prevalence, per million | 5.7 | 3.5 | 6.1 | |
| Proportion of newly diagnosed cases, % | 38 | 28 | 12 | |
| No. of newly diagnosed cases | 270 (210–400) | 130 (100–160) | 90 (70–110) | |
| Period incidence, per million | 2.1 | 1.0 | 0.7 | |
| BCS | No. of total cases (95% CI) | 280 (200–360) | 270 (190–360) | 410 (300–530) |
| Period prevalence, per million | 2.2 | 2.1 | 3.2 | |
| Proportion of newly diagnosed cases, % | 28 | 6 | 21 | |
| No. of newly diagnosed cases | 80 (60–100) | 16 (11–22) | 90 (60–110) | |
| Period incidence, per million | 0.6 | 0.1 | 0.7 |
CI, confidence interval.