Table 2.
Thirteen reported cases of primitive neuroectodermal tumor in the abdominal wall
| Ref. | Age | Sex | Size (cm) | Immuno-histo-chemistry | Molecular/cyto-genetic analysis | MATOD | Therapy | Follow-up | Relapse | Outcome |
| Roncati et al[9], 2015 | 45 yr | M | 1.5 | NSE, CD99 (+) | FISH (+) | NA | NA | NA | NA | NA |
| Riccardi et al[18], 2010 | 15 yr | M | 2.5-3.0 | CD99, NB84a, vimentin (+) | FISH, RT-PCR (-) | No | S + Ch | NA | NA | NA |
| Betal et al[19], 2009 | 61 yr | F | NA | CD99, CD56, cytokeratins, S100 (+) | NA | No | S + Ch (6 cycles of VDC) | NA | No | NA |
| Taylor et al[8], 2000 | 33 mo | M | 3.5 × 3.5 × 2.5 | CD99 (+) | NA | No | S | 10 yr | No | Survival |
| Soma et al[20], 2015 | 21 yr | F | 6 × 4 | CD 99, vimentin (+) | NA | No | S + Ch (VDC) | 6 mo | No | Survival |
| Somers et al[21], 2004 | 16 yr | F | 1.5 | CD99, CD56, S100 (+) | FISH and RT-PCR (-) | No | Before metastasis: S + Ch (6 cycles of VAC); after metastasis: S + RT + CT (1 cycle of IE + CBP) | NA | Yes | Death |
| Savić et al[22], 2017 | 15 yr | M | 3.8 × 2.6 × 3.7 | CD99, vimentin, synaptophysin (+) | RT-PCR (+) | No | S + Ch (VAC) + RT | 8m | No | Survival |
| Askri et al[23], 2008 | 35 yr | F | 6.5 × 4 | CD99 (+) | NA | NA | S + Ch (3 cycles of VDC ) | NA | NA | NA |
| Gurria et al[24], 2011 | 23 yr | F | 14 × 10 × 7 | CD99, PAS (+) | NA | No | S + RT + Ch (VAC/IE) | 8 mo | No | Survival |
| Aydinli et al[25], 2009 | 65 yr | M | 5 | CD99 (+) | NA | NA | S + Ch (6 cycles of VDCE) | 1 yr | No | Survival |
| Wang et al[26], 2017 | 21 yr | F | 5 × 4 | CD99, vimentin, NSE (+) | NA | Yes | S + RT + Ch (VAC) | 7 mo | Yes | Death |
| Zhan et al[27], 2012 | 2 yr | F | 5.0 × 3.8 × 5.1 | positive CD99, NSE, Ki67 (+) | NA | No | S + Ch (CTX + ADM + DDP) | 1 yr | No | Survival |
| Present case, 2019 | 66 mo | F | 3.4 × 6.1 × 2 | CD99, Syn (+) | NA | No | S + Ch (VDC/IE) | 66 mo | No | Survival |
+: Positive; MATOD: Metastatic at the time of diagnosis; S: Surgery; Ch: Chemotherapy; RT: Radiotherapy; NA: Not available; FISH: Fluorescence in situ hybridization; RT-PCR: Reverse transcription-PCR; VAC: Vincristine and actinomycin D, cyclophosphamide; IE: Ifosfamide and etoposide; VDC: Vincristine, doxorubicin, and cyclophosphamide.