Table 1. Clinical and laboratory characteristics of 10 patients with HS.
| Patient | Sex | Age | Family history | Hb (g/L) | Ret (%) | Spherocytes (%) | Hyperdense cells (%) | AGLT50 (s) | OF (g/L) (start-complete hemolysis) | EMA | Gallstone | Length × thickness of spleen (mm) |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 60 | y | 107 | 15.6 | 18 | 36 | 76 | 4.4–3.4; 6.0–4.6 (incubated) | no | + | 168×60 |
| 2 | F | 32 | Y | 55 | 19 | 16 | 46 | 69 | 4.4–3.4; 6.0–4.6 (incubated) | 4.5 | + | 135×46 |
| 3 | M | 30 | Y | 90 | 8.6 | 28 | 52 | 78 | 4.4–3.4; 6.0–4.6 (incubated) | no | + | 154×68 |
| 4 | F | 67 | Y | 94 | 5.6 | 30 | 48 | 200 | 4.2–3.4; 4.6–3.4 (incubated) | 4.5 | + | 150×45 |
| 5 | M | 40 | Y | 136 | 3,2 | 38 | 50 | 220 | 4.2–3.4; 4.6–3.4 (incubated) | 6.6 | + | 145×52 |
| 6 | M | 61 | Y | 68 | 8.6 | 46 | 60 | 98 | 4.4–3.4; 6.0–4.6 (incubated) | 5.84 | + | 210×88 |
| 7 | M | 67 | y | 143 | 9.2 | 32 | 40 | 120 | 4.4–3.4; 6.0–4.6 (incubated) | 7.52 | + | 176×65 |
| 8 | F | 63 | N | 100 | 3.2 | 17 | 64 | 90 | 5.0–3.8 | 6.69 | + | 188×69 |
| 9 | M | 46 | N | 90 | 8.9 | 68 | 80 | 160 | 4.4–3.4; 6.0–4.6 (incubated) | no | + | 172×68 |
| 10 | M | 48 | N | 85 | 1.1 | 18 | 38 | 200 | 4.2–3.4; 4.6–3.4 (incubated) | 5.86 | + | 138×35 |
Hb, hemoglobin; MCV, mean corpuscular volume; MCH, mean corpuscular hemoglobin; MCHC, mean corpuscular hemoglobin concentration; Ret, reticulocyte; IBIL, indirect bilirubin.