Table 1.
Causes of lymphadenopathy
| “The Big Five” |
| Tuberculosis |
| Lymphoma |
| Kaposi's sarcoma |
| HIV-ass. persistent generalized lymphadenopathy (PGL) |
| Reactive lymphadenitis in local infections |
| “The Rare Zebras” |
| Infectious |
| Atypical mycobacteriosis |
| Infectious mononucleosis (EBV) |
| Brucellosis |
| Tularemia |
| Syphilis |
| Cat-scratch disease |
| Fungal infections (e.g. histoplasmosis) |
| Toxoplasmosis |
| Inflammatory |
| Kikuchi-Fujimoto disease |
| Dermatopathic lymphadenitis |
| Rosai-Dorfman disease |
| Langerhans cell histiocytosis |
| Kimura disease |
| Sarcoidosis |
| Kawasaki's disease |
| Systemic lupus erythematosus |
| Malignant |
| Metastatic carcinoma |
| T-cell leukemia |
| Hairy-cell leukemia |
| Castleman's disease |
| Myeloid tumors |
| Others |
| Amyloidosis |
| Metabolic storage diseases |