Table III.
Review of published series consisting of at least 10 peripheral primary neuroectodermal tumor cases.
| Year of publication | No. of patients | Sex, M/F | Age, median, y | Size, mean, cm | Location (thoracopulmonary/abdomen and pelvis/paravertebral/head and neck/extremities) | LN | M | Treatment (combined/mono/no) | Survival | (Refs.) |
|---|---|---|---|---|---|---|---|---|---|---|
| 1983 | 15 | 5/10 | 21 | 8.8 | 2/1/1/2/9 | NR | 5 | NR | 2-year OS=36% | (10) |
| 1985 | 17 | 9/8 | 10 | NR | 11/1/0/2/3 | NR | 6 | 12/1/0; 4 NR | Median OS=17 m | (11) |
| 1988 | 42 | 28/14 | 15 | NR | 24/6/0/4/8 | NR | 10 | 29/3/0 (M0) | 3-year DFS (M0)=56% | (12) |
| 1989 | 10 | 8/2 | 32.6 | 8.8 | 0/0/0/1/9 | NR | 3 | 9/1/0 | 3-year OS=34% | (13) |
| 1989 | 26 | 15/11 | 14 | NR | 7/14/0/0/5 | NR | 16 | 24/2/0 | Median OS=21 m | (14) |
| 1991 | 36 | 23/13 | 15.2 | Uncertain | 17/9/0/1/8; 1 NR | NR | NR | 24/1/0; 11 NR | 3-year DFS=36% | (8) |
| 1991 | 54 | 31/23 | 17 | >5 (all) | 25/22/0/5/1; 1 NR | NR | 11 | NR | 5-year OS (M0)=21% | (15) |
| 1995 | 26 | 14/12 | Mean=9.8 | NR | 8/0/4/11/0; Other 3 NR | NR | 8 | NR | 2-year OS=65% | (16) |
| 1996 | 17 | 8/9 | 15.8 | NR | 1/6/2/3/5 | 1 | 6 | 17/0/0 | Median OS=40.8 m | (17) |
| 1998 | 26 | 11/15 | 1 | NR | 10/4/4/6/2 | NR | 4 | NR | OS=42% | (18) |
| 2001 | 13 | 8/5 | 15 | NR | 5/2/6/0/0 | NR | 1 | 12/1/0 | 3-year OS=68% | (19) |
| 2008 | 16 | 10/6 | 27 | 10.5 | 0/16/0/0/0/ | 2 | 4 | NR | 3-year OS=60% | (20) |
| 2009 | 25 | 15/10 | Mean: 27.2 | 10.2 | 25/0/0/0/0 | NR | NR | 22/3/0 | 3-year OS=56% | (21) |
| 2013 | 84 | 59/25 | 15 | Median: 9 | 84/0/0/0/0 | NR | 27 | 57/27/0 | 5-year OS=47.9% | (22) |
| 2013 | 23 | 14/9 | 29.5 | NR | 23/0/0/0/0/ | 4 | 0 | 23/0/0 | 5-year DFS=82% | (23) |
| 2014 | 36 | 25/11 | Mean: 30 | 8.1 | 8/6/4/6/12 | 3 | 0 | NR | 1-year OS=52% | (24) |
| 2017 | 18 | 15/3 | 36 | 7.2 | 0/18/0//0/0 | NR | NR | 3/11/4 | 1-year OS=33.3% | (25) |
| Present study | 89 | 43/46 | 25 | 12.6 | 25/41/7/7/9 | 17 | 16 | 46/35/8 | 3-year OS=32% |
M, male; F, female; LN, lymph nodes; M, metastasis; m, months; y, years; NR, not reported; OS, overall survival; DFS, disease free survival.