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. 2018 Jan 9;39(4):1755–1764. doi: 10.1002/hbm.23949

Table 1.

Participants’ demographic and clinical variables

HC FD
Age (mean ± SD) 42.1 ± 14.5 (range 19–70) 43.3 ± 12.2 (range 20–68)
Sex (M/F) 14/21 12/20
ERT n/a 29/32
ERT duration (mean ± SD) n/a 48.9 ± 50.1
Hyposmia n/a 3/32
Hypertension n/a 8/32
Arrhythmia n/a 1/32
Left ventricular hypertrophy n/a 23/32
Renal failure n/a 12/32
Proteinuria n/a 10/32
Nicotine dependence n/a 4/32
Acroparesthesia n/a 22/32
Neuropathy n/a 22/32
Cornea Verticillata n/a 29/32
Angiocheratoma n/a 30/32