Table 1.
Participants’ demographic and clinical variables
HC | FD | |
---|---|---|
Age (mean ± SD) | 42.1 ± 14.5 (range 19–70) | 43.3 ± 12.2 (range 20–68) |
Sex (M/F) | 14/21 | 12/20 |
ERT | n/a | 29/32 |
ERT duration (mean ± SD) | n/a | 48.9 ± 50.1 |
Hyposmia | n/a | 3/32 |
Hypertension | n/a | 8/32 |
Arrhythmia | n/a | 1/32 |
Left ventricular hypertrophy | n/a | 23/32 |
Renal failure | n/a | 12/32 |
Proteinuria | n/a | 10/32 |
Nicotine dependence | n/a | 4/32 |
Acroparesthesia | n/a | 22/32 |
Neuropathy | n/a | 22/32 |
Cornea Verticillata | n/a | 29/32 |
Angiocheratoma | n/a | 30/32 |