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. 2019 Nov 25;15:3273–3285. doi: 10.2147/NDT.S201862

Table 3.

Contraindications For Ketogenic Diet

Absolute Contraindications
Pyruvate carboxylase deficiency
Primary carnitine deficiency
Carnitine palmitoyltransferase I or II deficiency
Carnitinetranslocase deficiency
Medium chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
Long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
Short chain acyl dehydrogenase deficiency
Medium chain acyl dehydrogenase deficiency
Long chain acyl dehydrogenase deficiency
Short chain acyl dehydrogenase deficiency
Porphyria
Relative contraindications
Non compliance
Propofol use
Definite surgical focus of epilepsy

Note: Data from.7,8