Table 1.

Demographics of the 70 consecutively included KD patients. CAA status in acute phase was based upon echocardiography results

Demographics	n = 70	Remarks
Male	n = 55
Female	n = 15
Age in years at onset KD (median, range)	2.4 (0.12–16.91)	Age-at-onset was unknown in 2 patients.
Missed diagnosis, unknown treatment	n = 8	No treatment (IVIG/prednisone) received in 6 cases. Treatment in the acute phase was unknown in 2 others.
Treatment > 10 days after fever onset	n = 17
Treatment day (median, range)	8 (3–34)	Counted from the first day of fever until start of IVIG. In 2 patients, the only information available stated whether IVIG was given within or after 10 days of fever. In 4 patients, the day of treatment was unclear. In 8 patients, IVIG (or prednisone) was not administered.
Non-responder to 1st IVIG	n = 18	Persistent fever > 48 h after IVIG treatment.
Age in years at time of CT (median, range)	15.1 (0.48–59.45)
ΔTime in years (CT date–date of onset) (median, range)	11.7 (0.11–26.00)	Age-at-onset was unknown in 2 cases, which presented at adult age with myocardial infarction (MI).
CAA Z score acute stage: • Z score > 10 (giant) • Z score 3–10 (small- and medium-sized aneurysms) • Z score < 3 (no aneurysm) • Unknown	n = 27 n = 15 n = 26 n = 2