Table 1.
Baseline Demographic and Clinical Data of Study Group.
| Fontan (n = 25) | Atrial Septal Defect (n = 12) | |
|---|---|---|
| Age, y | 32.2 ± 9.1 | 28.6 ± 10.6 |
| Male, n (%) | 10 (40) | 3 (25) |
| Diagnosis, n (%) | ||
| Atrial Septal Defect | 0 (0) | 12 (100) |
| d-TGA | 5 (20) | 0 |
| Double Outlet RV | 5 (20) | 0 |
| Double Inlet LV | 4 (16) | 0 |
| Tricuspid Atresia | 4 (16) | 0 |
| Other | 7 (28) | 0 |
| Fontan Type, n (%) | ||
| Lateral Tunnel | 13 (52) | — |
| Extracardiac | 8 (32) | — |
| Atriopulmonary | 4 (16) | — |
| Central Venous Pressure, mmHg | 15.3 ± 4.9 | 7.6 ± 3.2 |
| Fontan Pressure, mmHg | 15.3 ± 5.0 | — |
| Presence of AVM n (%) | 10 (40) | 0 |
| History of PLE, n (%) | 1 (4) | 0 |
| Clinical Ascites, n (%) | 8 (32) | 0 |
| Liver Biopsy n (%) | ||
| Normal | 2 (8) | — |
| Fibrosis | 6 (24) | — |
| Cirrhosis | 4 (16) | — |
| Not Performed | 13 (52) | 12 |
| Arrhythmia within 6 months, n (%) | 5 (20) | 0 |
| History of Arrhythmia, n (%) | 18 (72) | 0 |
| Atrial Flutter | 10 (56) | — |
| Atrial Tachycardia | 5 (28) | — |
| Other | 2 (16) | — |
d-TGA, dextro-Transposition of Great Vessels; LV, Left Ventricle; RV, Right Ventricle; AVM, arteriovenous malformation; PLE, Protein-Losing Enteropathy.