Table 2.

Characteristics of the study 2 population

Characteristics of the Adult aHUS Cohort (January 1, 2007 to January 1, 2016)	Data
Total number of patients in the cohort	397
Female/male sex ratio	254/143
Age at time of aHUS onset (median yr [range])	29.3 (0.1–79.7)
Child-onset aHUS (%)	82 (20.6)
Age when entering the 2007–2016 cohort (median yr [range])	34.5 (18–79.7)
Complement/DGKE abnormality (%)	260 (65.5)
CFH	99 (24.9)
CFI	38 (9.6)
CFB	2 (0.5)
C3	40 (10.1)
MCP	45 (11.3)
DGKE	4 (1.0)
Combined CAP abnormalities	8 (2.0)
Anti-CFH antibody	24 (6.0)
Patients who reached ESKD before the end of the study period (%)	224 (56.4)
Death before the end of the study period (%)	39 (9.8)