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. 2008 Nov 1;23(11):1957–1972. doi: 10.1007/s00467-008-0872-4

Table 6.

Results of liver or combined liver and kidney transplantation in seven children with CFH mutations. Pre- and intra-operative intensive plasmatherapy appear as a prerequisite for success. PTLD post-transplant lymphoproliferative disease

Authors (reference) Age of patient (years) CFH mutation Transplantation Plasmatherapy Post-operative anticoagulation Outcome (follow-up)
Pre-operative Per-operative
Remuzzi et al. [68] 2 W 1183 R Liver + kidney No No No Liver failure at day 26; re-transplantation neurologic sequels
SCR 20
Cheong et al. [69] 2.5 C926 F Auxiliary liver No No No Death at 10 months from infections and PTLD
SCR 15
Remuzzi et al. [70] 2 E 1172 stop Liver + kidney No No No Primary non-function of liver, thrombotic/ischemic lesions, post-operative death)
SCR 20
Saland et al. ([71] and personal communication) 2.2 C 973 Y, SCR 15, V 1197 A, SCR 20 Liver + kidney PE 50 ml/kg FFP 19 ml/kg Yes Both grafts successful (4 years)
4 S 1191 L, SCR 20 Liver + kidney Idem Idem Yes Both grafts successful (1.5 years)
Jalanko et al. [72] 1.6 R 1215 Q Liver + kidney PE 98 ml/kg FFP 36 ml/kg Yes Both grafts successful (15 months)
SCR 20
16 R 1215 Q Liver + kidney PE 52 ml/kg at H-12 and 86 ml/kg pre-op PE 70 ml/kg Yes Both grafts successful (8 months)
SCR 20