| ER | Endoplasmic Reticulum |
| UPR | Unfolded Protein Response |
| IRE1 | Inositol-requiring enzyme 1 α |
| PERK | Protein kinase R (PKR)-like endoplasmic reticulum kinase |
| ATF6 | Activating transcription factor 6 |
| ERAD | Endoplasmic-reticulum-associated protein degradation |
| EGAD | Endosome and Golgi-related stress-responsive Associated Degradation |
| XBP1 | X-Box binding protein 1 |
| ATF4 | Activating transcription factor 4 |
| eiF2α | Eukaryotic translation initiation factor 2A |
| ERGIC | ER-to-Golgi intermediate compartment |
| ERES | ER exit sites |
| HSPs | Heat shock protein |
| GRP78 | Glucose-regulated protein 78 |
| CANX | Calnexin |
| CALR | Calreticulin |
| Pre-QC | Pre empty-Quality Control |
| PDI | Protein Disulfide Isomerases |
| PPI | Peptidyl-Prolyl cis–trans isomerases |
| PTM | Post Translational Modification |
| EDEM | ER degradation-enhancing alpha-mannosidase-like protein |
| PD | Parkinson’s disease |
| HD | Huntington’s disease |
| AD | Alzheimer’s disease |
| CMT | Charcot-Marie-Tooth neuropathies |