ER |
Endoplasmic Reticulum |
UPR |
Unfolded Protein Response |
IRE1 |
Inositol-requiring enzyme 1 α |
PERK |
Protein kinase R (PKR)-like endoplasmic reticulum kinase |
ATF6 |
Activating transcription factor 6 |
ERAD |
Endoplasmic-reticulum-associated protein degradation |
EGAD |
Endosome and Golgi-related stress-responsive Associated Degradation |
XBP1 |
X-Box binding protein 1 |
ATF4 |
Activating transcription factor 4 |
eiF2α |
Eukaryotic translation initiation factor 2A |
ERGIC |
ER-to-Golgi intermediate compartment |
ERES |
ER exit sites |
HSPs |
Heat shock protein |
GRP78 |
Glucose-regulated protein 78 |
CANX |
Calnexin |
CALR |
Calreticulin |
Pre-QC |
Pre empty-Quality Control |
PDI |
Protein Disulfide Isomerases |
PPI |
Peptidyl-Prolyl cis–trans isomerases |
PTM |
Post Translational Modification |
EDEM |
ER degradation-enhancing alpha-mannosidase-like protein |
PD |
Parkinson’s disease |
HD |
Huntington’s disease |
AD |
Alzheimer’s disease |
CMT |
Charcot-Marie-Tooth neuropathies |